Prion disease update 2012

A ProMED-mail post
The number of deaths due to definite or probable vCJD as of Mon 6 Aug
2012 remains 176. No definite/probable patient remains alive, so the
total number of definite or probable vCJD cases (dead and alive) remains 176.

The overall picture remains consistent with the view that the vCJD
outbreak in the UK is in decline, albeit now with a pronounced tail.
The 1st cases were observed in 1995, and the peak number of deaths was
28 in the year 2000, followed by 20 in 2001, 17 in 2002, 18 in 2003, 9
in 2004, 5 in 2005, 5 in 2006, 5 in 2007, one in 2008, 3 in 2009, 3 in
2010, 5 in 2011, and none so far in 2012.

Totals for all types of CJD cases in the UK in 2012
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During 2012 so far [as of 6 Aug 2012], there have been 58 referrals,
38 fatal cases of sporadic CJD, one case of GSS
[Gerstmann-Straussler-Scheinker disease], 3 cases of familial CJD, no
cases of vCJD or of iatrogenic CJD.

Since records began in 1990, there have been 2946 referrals, 1345
fatal cases of sporadic CJD, 176 cases of vCJD, 97 cases of familial
CJD, 68 cases of iatrogenic CJD, and 47 cases of GSS.